ZFIN is now using GRCz12tu for Genomic Data
Gene

runx2b

ID
ZDB-GENE-040629-4
Name
RUNX family transcription factor 2b
Symbol
runx2b Nomenclature History
Previous Names
None
Type
protein_coding_gene
Location
Chr: 20 Mapping Details/Browsers
Genome Assembly
GRCz12tu
Annotation Status
Current
Description
Enables DNA-binding transcription factor activity and nuclear vitamin D receptor binding activity. Acts upstream of or within dorsal/ventral pattern formation; positive regulation of DNA-templated transcription; and skeletal system development. Predicted to be located in cytosol and nucleoplasm. Predicted to be active in nucleus. Is expressed in several structures, including EVL; dermis; fin; pharyngeal arch; and skeletal system. Human ortholog(s) of this gene implicated in cleidocranial dysplasia; lung non-small cell carcinoma; metaphyseal dysplasia-maxillary hypoplasia-brachydactyly syndrome; and osteonecrosis. Orthologous to human RUNX2 (RUNX family transcription factor 2).
Genome Resources
Note
None
Comparative Information
Expression
All Expression Data
97 figures from 74 publications
Cross-Species Comparison
High Throughput Data
Thisse Expression Data
No data available
Wild Type Expression Summary
Phenotype
All Phenotype Data
4 figures from 3 publications
Cross-Species Comparison
Alliance
Phenotype Summary
Mutations
Mutants
Sequence Targeting Reagents
Human Disease
Associated With runx2b Human Ortholog
Disease Ontology Term Multi-Species Data OMIM Term OMIM Phenotype ID
cleidocranial dysplasia Alliance Cleidocranial dysplasia 119600
cleidocranial dysplasia Alliance Cleidocranial dysplasia, forme fruste, dental anomalies only 119600
cleidocranial dysplasia Alliance Cleidocranial dysplasia, forme fruste, with brachydactyly 119600
metaphyseal dysplasia-maxillary hypoplasia-brachydactyly syndrome Alliance Metaphyseal dysplasia with maxillary hypoplasia with or without brachydactyly 156510
Associated With runx2b Via Experimental Models
No data available
Gene Ontology
Protein Domains
Domain, Family, and Site Summary
Type InterPro ID Name
Domain IPR013524 Runt domain
Domain IPR013711 Runx, C-terminal domain
Family IPR000040 Acute myeloid leukemia 1 protein (AML1)/Runt
Family IPR016554 Runt-related transcription factor RUNX
Homologous_superfamily IPR008967 p53-like transcription factor, DNA-binding domain superfamily
Homologous_superfamily IPR012346 p53/RUNT-type transcription factor, DNA-binding domain superfamily
Homologous_superfamily IPR027384 Runx, central domain superfamily
Domain Details Per Protein
Protein Additional Resources Length Acute myeloid leukemia 1 protein (AML1)/Runt p53-like transcription factor, DNA-binding domain superfamily p53/RUNT-type transcription factor, DNA-binding domain superfamily Runt domain Runt-related transcription factor RUNX Runx, central domain superfamily Runx, C-terminal domain
UniProtKB:A0A8M1PMM2 InterPro 464
UniProtKB:A0A8M9PSK4 InterPro 323
UniProtKB:A0AB32T894 InterPro 646
UniProtKB:A0AB32T8Z6 InterPro 619
UniProtKB:A0AB32TA58 InterPro 501
UniProtKB:A0AB32TDW2 InterPro 502
UniProtKB:A0AC58I2B8 InterPro 646
UniProtKB:A0AC58I2B9 InterPro 646
UniProtKB:A0AC58I2C1 InterPro 615
UniProtKB:A0AC58I2C4 InterPro 646
UniProtKB:A0AC58I2C6 InterPro 603
UniProtKB:A0AC58I2C8 InterPro 603
UniProtKB:A0AC58I2D0 InterPro 505
UniProtKB:A0AC58I2D1 InterPro 603
UniProtKB:A0AC58I2D2 InterPro 603
UniProtKB:A0AC58I2D3 InterPro 502
UniProtKB:A0AC58I2D4 InterPro 502
UniProtKB:A0AC58I2D5 InterPro 502
UniProtKB:A0AC58I2D7 InterPro 502
UniProtKB:A0AC58I2D8 InterPro 615
UniProtKB:A0AC58I2D9 InterPro 502
UniProtKB:A0AC58I2E0 InterPro 502
UniProtKB:A0AC58I2E2 InterPro 502
UniProtKB:A0AC58I2E3 InterPro 502
UniProtKB:A0AC58I2E4 InterPro 502
UniProtKB:A0AC58I2E5 InterPro 502
UniProtKB:A0AC58I2E6 InterPro 502
UniProtKB:A0AC58I2E7 InterPro 615
UniProtKB:A0AC58I2E8 InterPro 361
UniProtKB:A0AC58I2E9 InterPro 462
UniProtKB:A0AC58I2F0 InterPro 360
UniProtKB:A0AC58I2F1 InterPro 502
UniProtKB:A0AC58I2F4 InterPro 502
UniProtKB:A0AC58I2F5 InterPro 502
UniProtKB:A0AC58I2G0 InterPro 502
UniProtKB:A0AC58I2I0 InterPro 615
UniProtKB:A0AC58I2J0 InterPro 502
Transcripts
Genome Browsers
Type Name Annotation Method Has Havana Data Length (nt) Analysis
mRNA runx2b-201 (1) Ensembl 1,707 nt
mRNA runx2b-202 (1) Ensembl 1,533 nt
mRNA runx2b-203 (1) Ensembl 1,128 nt
mRNA runx2b-204 (1) Ensembl 675 nt
mRNA runx2b-205 (1) Ensembl 2,491 nt
Interactions and Pathways
No data available
Antibodies
No data available
Plasmids
No data available
Constructs
Marker Relationships
Sequences
Genome Browsers
Orthology
Comparative Orthology
Alliance
Gene Tree
Ensembl
Citations