PUBLICATION

LOXHD1b knockout alters swimming behavior in zebrafish

Authors
Asaoka, Y., Tarumoto, S., Hirose, Y., Iwamoto, A., Tokunaga, M., Matsuura, T., Takemoto, Y., Yamashita, H., Furutani-Seiki, M., Sugahara, K.
ID
ZDB-PUB-251011-1
Date
2025
Source
Cell and tissue research   402: 243-254 (Journal)
Registered Authors
Sugahara, Kazuma
Keywords
Hereditary deafness, LOXHD1b, Lateral line, Swimming behavior, Zebrafish
MeSH Terms
  • Animals
  • CRISPR-Cas Systems/genetics
  • Gene Knockout Techniques*
  • Hair Cells, Auditory/metabolism
  • Humans
  • Larva
  • Lateral Line System/metabolism
  • Swimming*/physiology
  • Zebrafish*/genetics
  • Zebrafish*/physiology
  • Zebrafish Proteins*/genetics
  • Zebrafish Proteins*/metabolism
PubMed
41071356 Full text @ Cell Tissue Res.
Abstract
Since human inner ear hair cells do not regenerate, the current treatments of hereditary deafness depend on hearing aids or cochlear implant. However, uncovering the functions of genes responsible for hereditary hearing loss is not only useful for their diagnosis but also for developing therapies. The pathogenetic mechanism of human non-syndromic deafness DFNB77 without morphological defects in the inner year caused by LOXHD1 mutations is not fully understood. We introduced zebrafish because the lateral line hair cells are structurally and physiologically similar to the human inner ear hair cells and mutations involved in non-symptomatic hearing loss can be assessed by their swimming behavior. The knock-out (KO) of LOXHD1b gene which is expressed in the lateral line hair cells was generated using the CRISPR-Cas9 system in zebrafish, and its morphological and functional changes were evaluated. As with human patients the LOXHD1b KO zebrafish larvae did not exhibit detectable morphological defects, but showed prolonged water flow sensing time. These results suggest that LOXHD1b plays pivotal roles for the hair cell neural activity and its KO zebrafish mutant serves as a useful model for revealing the molecular mechanisms linking LOXHD with hair cell function and for a drug screening to rescue the swimming phenotype.
Genes / Markers
Figures
Show all Figures
Expression
Phenotype
Mutations / Transgenics
Human Disease / Model
Sequence Targeting Reagents
Fish
Antibodies
Orthology
Engineered Foreign Genes
Mapping